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In patulous eustachian tube (pET) dysfunction, the eustachian tube stays open most of the time. The eustachian tube is a passageway from the back of the nose to the middle ear that may be opened or closed by action of a valve-like device. Under normal circumstances, it remains closed for most of the day, opening only on occasion to equalize air pressure in the middle ear and the exterior environment.
If the tube remains open, the patient complains of hearing one's own voice or one's breathing as too loud (autophony), hearing echoes of one's own voice, or hearing ocean waves much like the sound produced by holding a shell over one's ear.
The condition is benign but may generate, over time, serious and even extreme responses to the abnormal sounds.
Symptoms of pET include variable intensity of the sensation of fullness in the ear; oceanic roaring sounds associated with breathing; loud, echoing sensations and a sense of hearing one's own speech at a high volume. There may also be a stopped-up feeling in the ear.
Dizziness may, on occasion, accompany the abnormal sound sensations. The heightened sounds of chewing may be loud enough to interfere with eating.
Patulous eustachian tube results when the eustachian tube is open continuously or for long periods. Under normal conditions, the eustachian tube remains closed because the natural elasticity of the structure tends towards closure or because of surface tension of the interior of the tube (lumen) and pressure by the muscles outside the tube. If any (or all) of these forces fail, the tube does not close.
For reasons that are not clear, the condition is often associated with recent weight loss, and with a high concentration of estrogens in the blood due to pregnancy or medication. Other possible causes of pET dysfunction are neuromuscular disorders such as multiple sclerosis, poliomyelitis, Parkinson's disease and neurovascular accident. Adhesions and scarring of the pharyngeal recess and of the posterior lip of the pharyngeal opening of the eustachian tube can also result in the disorder.
Patulous eustachian tube is most prevalent in women who have had a significant recent weight loss and in pregnant women. Adults and adolescents are most often affected. Instances of this occurring among children are very rare.
Various epidemiological studies suggest that the incidence of the condition in the general population is 0.3% to 6.6%. Of those affected however, only about 20% seek medical treatment.
Middle Ear Effusion is the chronic accumulation of thick fluid in the middle ear. Deafness, fullness and crackling noises in the ears can occur as a result of this disorder.
A clinical history and patient description of the symptoms are often sufficient for the diagnosis. There are several tests that may be used to confirm the diagnosis, including the detection of movement of the ear drum along with respiration, (tympanometry) and others.
Temporary relief may be achieved by having the affected person lie down or bend forward with the head between the knees. Sniffing can also provide momentary relief.
In some cases, estrogen-based nasal drops or anticholinergics may be effective. Weight gain may also cause pET to recede.
Information on current clinical trials is posted on the Internet at www.clinicaltrials.gov. All studies receiving U.S. government funding, and some supported by private industry, are posted on this government web site.
For information about clinical trials being conducted at the NIH Clinical Center in Bethesda, MD, contact the NIH Patient Recruitment Office:
Tollfree: (800) 411-1222
TTY: (866) 411-1010
For information about clinical trials sponsored by private sources, contact:
Patulous eustachian tube dysfunction has been treated surgically by cutting the hook around which the tendon of the tensor veli palatini muscle passes (pterygoid hamulotomy) combined with transposition or transection of the tendon of this muscle. Good results have been obtained in approximately 70 percent of persons undergoing this procedure.
The drug Patul-end has received an orphan drug designation for its use in the treatment of patulous eustachian tube. More studies are needed to determine the long-term safety and effectiveness of this drug for the treatment of patulous eustachian tube. For more information, contact:
Ear Foundation (of Santa Barbara)
2420 Castillo Street
Santa Barbara, CA 93105-5307
Telephone: (805) 563-1111
Fax: (805) 563-2277
11730 Plaza America Drive, Suite 300
Reston, VA 20190
Phone #: 703-790-8466
800 #: 800-222-2336
Home page: http://www.audiology.org
310 W. Lake St.
Elmhurst, IL 60126 USA
Phone #: 630-617-5079
800 #: --
Home page: http://www.american-hearing.org/
1444 I Street NW
Washington, DC 20005 United States
Phone #: 202-449-1100
800 #: 800-327-9355
Home page: http://www.betterhearing.org
2420 Castillo Street
Santa Barbara, CA 93105-4346
Phone #: 805-569-1111
800 #: N/A
Home page: http://earfdn.org/index.htm
PO Box 8126
Gaithersburg, MD 20898-8126
Phone #: 301-251-4925
800 #: 888-205-2311
Home page: http://rarediseases.info.nih.gov/GARD/
31 Center Drive, MSC 2320
Bethesda, MD 20892-3456
Phone #: 301-402-0900
800 #: 800-241-1044
Home page: http://www.nidcd.nih.gov
6700 Washington Avenue South
Eden Prairie,, MN 55344 United States
Phone #: 866-354-3254
800 #: 800-648-4327
Home page: http://www.sotheworldmayhear.org/
Ballenger JJ, ed. Diseases of the Nose, Throat, Ear, Head and Neck. 14th ed. Lea & Febiger, Malvern, PA; 1991:1101-02.
Kano S, Kawase T, Baba Y, et al. Possible new assessment of patulous eustachian tube function: Audiometry or tones presented in the nasal cavity. Acta Otolaryngol. 2004;124:431-35.
Yoshida H, Kobayashi T, Morikawa M, et al. CT imaging of the patulous eustachian tube - comparison between sitting and recumbent positions. Auris Nasus Larynx. 2003;30:135-40.
Doherty JK, Slattery WH 3rd. Analogous fat grafting for the refractory patulous eustachian tube. Otolaryngol Head Neck Surg. 2003;128:88-91.
Poe DS, Abou-Halawa A, Abdel-Razek O. Analysis of the dysfunctional eustachian tube by video endoscopy. Otol Neurotol. 2001;22:590-95.
Kaneko A, Hosoda Y, Doi T, et al. Tubal compliance - changes with age and tubal malfunction. Auris Nasus Larynx. 2001;28:121-24.
Tideholm B, Carlborg B, Brattmo M. Continuous long-term measurements of the middle ear pressure in subjects with symptoms of patulous eustachian tube. Acta Otolaryngol. 1999;119:809-15.
Chen DA, Luxford WM. Myringotomy and tube for relief of patulous eustachian tube symptoms. Am J Otol. 1990;11:272-73.
Robinson PJ, Hazell JW. Patulous eustachian tube syndrome: the relationship with sensorineural hearing loss. Treatment by eustachian tube diathermy. J Laryngol Otol. 1989;103:739-42.
FROM THE INTERNET
Patulous Eustachian Tube. emedicine. Last updated: August 6, 2002. 7pp.
Own Voice Sounds Distorted & Loud. IVillage. nd. 2pp.
Kuppersmith RB. Eustachian Tube Function and Dysfunction. Grand Rounds Archives. The Bobby R. Alford Department of Otorhinolaryngology and Communicative Sciences. Baylor College of Medicine. July 11, 1996. 11pp.
Report last updated: 2008/03/17 00:00:00 GMT+0