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Prune Belly Syndrome

Abstract

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Synonyms of Prune Belly Syndrome

  • Abdominal Muscle Deficiency Syndrome
  • Congenital Absence of the Abdominal Muscles
  • Deficiency of abdominal musculature
  • Eagle-Barrett Syndrome
  • Obrinsky Syndrome
  • Triad syndrome

Disorder Subdivisions

  • No subdivisions found.

General Discussion

Prune-Belly syndrome, also known as Eagle-Barrett syndrome, is a rare disorder characterized by partial or complete absence of the stomach (abdominal) muscles, failure of both testes to descend into the scrotum (bilateral cryptorchidism), and/or urinary tract malformations. The urinary malformations may include abnormal widening (dilation) of the tubes that bring urine to the bladder (ureters), accumulation of urine in the ureters (hydroureter) and the kidneys (hydronephrosis), and/or backflow of urine from the bladder into the ureters (vesicoureteral reflux). Complications associated with Prune-Belly syndrome may include underdevelopment of the lungs (pulmonary hypoplasia) and/or chronic renal failure. The exact cause of Prune-Belly syndrome is not known.

Prune Belly Syndrome Resources

Organizations:

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