Ichthyosis, Erythrokeratolysis Hiemalis
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Synonyms of Ichthyosis, Erythrokeratolysis Hiemalis
- Disorder of Cornification 19 (Erythrokeratolysis Hiemalis)
- DOC 19
- Erythrokeratolysis Hiemalis
- Keratolytic Winter Erythema
- Oudtshoorn Skin
- No subdivisions found.
Erythrokeratolysis hiemalis is an extremely rare form of ichthyosis that was first described in South Africa but has subsequently been identified in other countries. In such cases, a link to South Africa has been determined. The disorder is characterized by periodic attacks of red (erythematous) plaques that are distributed equally on both sides of the body. A layer of skin can be peeled from these plaques. Symptoms usually improve with age. The disorder tends to become worse with the cold weather.
Organizations related to Ichthyosis, Erythrokeratolysis Hiemalis
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