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Ichthyosis, Erythrokeratolysis Hiemalis

Abstract

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Synonyms of Ichthyosis, Erythrokeratolysis Hiemalis

  • Disorder of Cornification 19 (Erythrokeratolysis Hiemalis)
  • DOC 19
  • Erythrokeratolysis Hiemalis
  • Keratolytic Winter Erythema
  • Oudtshoorn Skin

Disorder Subdivisions

  • No subdivisions found.

General Discussion

Erythrokeratolysis hiemalis is an extremely rare form of ichthyosis that was first described in South Africa but has subsequently been identified in other countries. In such cases, a link to South Africa has been determined. The disorder is characterized by periodic attacks of red (erythematous) plaques that are distributed equally on both sides of the body. A layer of skin can be peeled from these plaques. Symptoms usually improve with age. The disorder tends to become worse with the cold weather.

Ichthyosis, Erythrokeratolysis Hiemalis Resources

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