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Ichthyosis, Erythrokeratodermia Variabilis

Abstract

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NORD is very grateful to the members of the Medical and Scientific Advisory Board of the Foundation for Ichthyosis & Related Skin Types for assistance in the preparation of this report.

Synonyms of Ichthyosis, Erythrokeratodermia Variabilis

  • EKV
  • Keratosis Rubra Figurata
  • Mendes Da Costa Syndrome

Disorder Subdivisions

  • No subdivisions found.

General Discussion

Erythrokeratodermia variabilis is an inherited skin disorder characterized by two features: short-lasting red patches in various sizes and shapes that may involve any part of the body; and thickening of the skin (hyperkeratosis). The hyperkeratosis can either be generalized, or localized as fixed, sharply defined, thickened plaques. The hyperkeratosis may also involve the skin of the palms and soles. Skin lesions are made worse by sudden changes in temperature and friction. The red patches may be accompanied by a burning sensation.

Organizations related to Ichthyosis, Erythrokeratodermia Variabilis

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